RETROPERITONEAL NODAL APLASIA, ASPLENIA, CHYLOUS EFFUSION AND LYMPHATIC DYSPLASIA: AN ACQUIRED IMMUNODEFICIENCY SYNDROME?

L Carini, LD Meregaglia, C Galli, G Segalini, M Strada, J Jones, MH Witte, CL Witte

Abstract


Two adult patients (one in Italy and the other in
the USA) are described with similar findings of
paraaortic nodal aplasia, asplenism, multiple serous
and chylous effusions, and retroperitoneal lymphatic
dysplasia. Although the clinical courses are incomplete,
this unusual constellation of signs in the
setting of normal peripheral lymph trunks suggest an
acquired rather than inborn anomaly and possibly a
variant acquired immunodeficiency syndrome.


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